Porokeratotic eccrine ostial and dermal duct nevus: A medical case

Abstract

Porokeratotic eccrine ostial and dermal duct nevus is a rare adnexal hamartoma, characterized by keratotic papules that exhibit comedo-like openings presenting in a linear disposition. It’s a rare condition, fewer than 70 cases have been reported. Nowadays its considered in the adnexal ostium nevi group. Its importance lays on the somatic mutation found on the nevi tissue, which is similar to the keratitis-ichthyosis-deafness (KID) syndrome, meaning that there is a possibility this mutation can be inherited or passed down to the offspring, with the consequent risk of developing KID syndrome.