Congenital Smooth Muscle Hamartoma. Report of a case and brief review of the literature.

Abstract

Congenital hamartoma of smooth muscle is a benign proliferation, generally solitary of smooth muscle, quite rare and predominantly in males. It is usually located in the trunk or in the root of the limbs with variable degree of pigmentation and hypertrichosis, sometimes presenting positivity of the so called pseudo Darier’s sign. We present the case of a 2 year old girl with a lesion on her left knee present since birth and we make a small review of the literature on the subject.