Pigmented dermatofibrosarcoma protuberans, Bednar tumor: Case report and Dermatoscopic findings

Abstract

Pigmented dermatofibrosarcoma protuberans, or Bednar tumor (BT) accounts for 1% of DFSP cases. It is a low-intermediate grade connective tissue neoplasm, characterized by slow growth, and a high tendency to local recurrence. Its etiology is related to a genetic alteration that affects the platelet-derived growth factor beta and the collagen type 1 alpha 1 gene, generating the COL1A1-PDGFB fusion gene. There are few Dermatoscopic reports describing its pigmented variant. A clinical case of Bednar tumor is presented, along with its Dermatoscopic findings.