Reticulate acropigmentation of Kitamura: Clinical case report

Abstract

Reticulate Acropigmentation of Kitamura (RAK) is a rare autosomal dominant genodermatosis with variable penetrance. A prevalence of less than one per 100,000 is observed; to date there are only 130 published cases.

Lesions appear as slightly depressed lentiginous and hyperpigmented macules with reticular arrangement, located on the dorsal side of the hands and feet. Over time, they may extend proximally as they become hyperpigmented, proportionally to the time of evolution and sun exposure.

Diagnosis is based on family, clinical and histopathological pathological medical history.

So far there are no defined criteria for this disease, so exhaustive studies and complementary tests must be carried out.

A 16-year-old female patient presents with 2-week hyperpigmented brownish macules located on the right hand, which progressively spread to the contralateral hand. These lesions, of reticulated appearance, have affected the dorsum of the 1st, 2nd and 3rd finger of both hands, symmetrically and bilaterally, extending to the wrists. RAK was considered. Histopathology finally confirmed its diagnosis.